Dandy Walker syndrome: shuruudaha dhacdo, calaamadaha, daaweynta iyo saadaasha muuqaalada

Waqtigan xaadirka ah, nuurka u muuqataa badan oo carruurta ku dhalatay cudur. Mid ka mid ah dhibaatooyinka ugu adag oo halis ah waa Dandy Walker syndrome.

Sababaha ugu waaweyn ee aan caadi ahayn ee lagu dhasho ee soo socda:

1. Inta badan khubaro ku andacoonayaan in ay tahay a cudur la iska dhaxlo, kaas oo la hiddo goostay. Arrintan waxa xaqiijiyay heli karaa tirakoobka culuumta caafimaadka.
2. Dandy Walker midho logu waxay badanaa ka dhacdaa kuwa hooyooyinka ay dhibaatadu ka Khamriga chronic. Iyo, maqnaanayo laga yaabaa xataa aan caadi ahayn kale ee la xiriira hidde ee ilmaha. ka xaqiiqda ah in jidhka dumarka cabbo ma aha jawi wanaagsan ee horumarka ah ee ilmaha caloosha ku reebo, ay inta badan qaadataa aad darro, waayo, dhalista. Sidaa darteed, Dandy Walker syndrome in ilmo yar waxaa inta badan laga helay oo kaliya uu ku dhashay ka dib markii.
3. diabetes hiddo-keena, rubella, cudurka cytomegalovirus in haweenka uurka leh - ayaa sidoo kale sababaha halista horumarka la yaab this.

Dandy Walker syndrome loogu ogaan karaa calaamadaha soo socda.

Calaamadaha ugu horeeya waxaa suurtagal ah in la ogaado in ay laba iyo labaatan asbuuc. On baaritaan ultrasound hore pathognomonic, astaamaha caadiga ah, kaas oo ka mid ah:

• joogitaanka of fiix ee gobolka of fossa (aagga taangiyada waaweyn)
• aplasia ama hypoplasia ah vermis cerebellar;
• ventricle afaraad balaartay.

Masraxa weyn ee uurka noqdaan calaamado cad oo la arki karo:

• "Dhanxanegga dillaacii" ;
• "Dillaacii dibinta";
• cillado lagu dhasho kelyaha,
• syndactyly - isuga ee faraha on addimada ah.

Dandy Walker syndrome bilaabaa in uu si deg deg ah kadib dhalmada. Tani waa run gaar ah calaamadaha dareemayaasha daran, darnaanta waa ka variable. Si dhakhso ah, calaamadaha sida hypertension intracranial iyo yiraahdo hydrocephalus.

Ilmo qaba cudurada waa mid aad u deganaan la'aan, waxaa ka danbayso in horumarka, labada jireed iyo maskaxeed-dareemayaasha. calaamadaha cerebellar ayaa sidoo kale ahbaa - xanuunada isuduwidda, xaalad muruqa caydi iyo ataxia.

DendiUokera syndrome. Daaweynta iyo ogaanshaha

Statement of baaritaanada hooyada - "Midhaha syndrome Dandy Walker" - hore ee aabbihiis iyo hooyadiis dhigeysa dhibaato aad u daran. Waxaad u baahan tahay in ay go'aan ka - inaad xajisaan oo midho leh jaaniska boqolkiiba 100 ilmaha jiran a, ama uurka la joojiyo. Sida caadiga ah, dhakhaatiirta talabixiya labaad.

Iyadoo ay taasi jirto, caruurta la foomkan cudurka si joogto ah u dhashay. Daaweynta in ay taasi dhacdo waa mid aad u xun oo waxaa inta badan aan waxtar lahayn.

Laakiin qaliinka waxaa loo isticmaalaa marka foomka aan dhamaystirnayn oo cudurada iyo yiraahdo hydrocephalus. Qaadashada isku tallaalidda ventricle ah lateral iyo cyst ah ma awoodo inuu baabi'iyo dhaawac maskaxda ah. Ilmuhu wuxuu u koraan lahaa neuropsychiatric naafada leh dhibaatooyin jidheed oo daran, tiro ka mid ah cudurada la xiriira, iyo deficiency maskaxda.

Saadaasha horumarka carruurta cillad-this

Saadaasha horumarka carruurta qaba Dandy Walker syndrome fadhiya, aad u allifey. Sida caadiga ah, si tartiib ah u sii kordhaya decompensation cerebral. Haddii ay sidaa tahay, haddii ay jirto qaab daran cudurka iyo la'aanta ah ee dhawrid caafimaad oo ku habboon, bukaanka sida dhinto ee lixda bilood ee ugu horreeya ee nolosha. Sida laga soo xigtay tirakoob, waa boqolkiiba konton.

Inta kale ee carruurta, xitaa haddii ay jirto shaqo halis ah oo dhakhaatiirta iyo waalidiintu waa kuwo wax badan ka danbeeya in ay horumarka, tan iyo heerka sirdoonka ay leeyihiin oo aad u yar yahay (aan suurtogal ah inuu u soo kabsado ka dib on). Intaa waxaa dheer, waxaa jira functional ah calaamadeeyay xaaladda maskaxda ah.