Caafimaadka, Cudurrada iyo Xaaladaha
Ehlers Danlos Syndrome,
Ehlers-Danlos syndrome - ugu badan dhaxlay
cudurka unugyo. dhacdooyinka ka mid yahay kiiska
a boqol oo kun oo dhalatay. Under group syndrome weheliso this
cudurada taas oo ku salaysan yihiin collagen iin kuwaas oo asaas u
unugyo. Waxaa la siiyaa in ka badan toban nooc oo cudurka, kala duwan ee dhinacyada qaar ka mid ah. calaamadaha dibadda in ay leeyihiin Ehlers-Danlos syndrome, ayaa muujiyay in extensibility kordhay, nuglaanta maqaarka, dhaqdhaqaaqa xubnaha iyo calaamadaha diathesis hemorrhagic. Waxa kale oo jira soo gaartay ee habka neefsashada iyo nidaamka wadnaha iyo, habka muruqyada, mareenka caloosha iyo mindhicirka.
maqaarka ee bukaanka qaba cudurka of Ehlers Danlos syndrome, jilicsan, khafiif ah, liidata go'an in unugyada ku lammaan. At dhaawac ugu yar ee dillaaciddu maqaarka hardhealed dhacaan, goobta halkaas oo nabaro xagtin la aasaasay oo dushiisuna waanuu. Syndrome Ehlers -Danlosa lagu gartaa dhaqdhaqaaqa aan caadi ahayn oo ka mid ah kala-goysyada, kuwaas oo natiijada baxa chronic iyo subluxations kalagoysyada. Xaaladaha badankooda cudurka waxaa ku weheliyay diathesis hemorrhagic, in bukaanka qaba nabaro fudud iyo hematoma muuqan deegaamaynta kala duwan. dhiig caadiga ah ka mareenka caloosha iyo mindhicirka, cirridka, ilmo galeenka.
Waayo, qaar ka mid ah cudurada waxaa lagu gartaa go'idda iyo ilmo
jallo. Ehlers syndrome - Danlos syndrome waxaa mararka qaarkood la socda khalad
formation of ilkaha iyo maqnaanshaha qayb ahaan, horumarinta periodontitis.
Xadgudubyada nidaamka muruqyada yihiin muujiyey in foomka of lahayo ku of xabadka
unugyada iyo dhaf-dhabarta. Bukaan-socodka waxaa inta badan Sheelada helay
deegaamaynta kala duwan. Iyadoo guuldarro oo ka mid ah xubnaha gudaha ku xanuunsado wadnaha
weelal, nidaamka bronchopulmonary, aneurysms vascular loo sameeyay badan
maskaxda iyo quseyo. Iyadoo guuldarro wadnaha loo sameeyay mada kala duwan.
Ehlers-Danlos Syndrome Daaweynta
waxbarashada kala duwan ku qaadeen for ogaanshaha sax ah oo cudurka in
xarumaha bukaan-jiifka gaar ah. Keena dhibaatooyin weyn
dhibaatooyin uurreyda iyo umulaha iyo qalliinka bukaan ah kuwaas oo laga helay syndrome ah
Ehlers-Danlos syndrome. Daaweynta waxaa si toos ah ugu horayn in xasilinta iyo
caadiga ah geeddi socodka dheefshiidka ee habdhiska dhexe iyo nidaamka wadnaha iyo,
nidaamka socon karto. Therapy cudurka waxaa ka mid ah
soo dhaweyn tiro balaadhan oo ah fitamiinada B, A iyo E. natiijada Good siin
carboxylase iyo ascorbic acid, irbado ee hormone koritaanka (somatotropin
hormone) chloride carnitine. Bukaan-socodka talinayaa daawada in kor loogu qaado waxqabadka maskaxda (Pantogamum, Nootropilum, Riboxinum, rutin, Pananginum). Ka sokow waxaa lagama maarmaan ah in la qabto daaweynta sida daaweynta dabiiciga ah si joogto ah sida irbadaha laser, therapy magnetic. Bukaan-socodka ayaa sidoo kale qori kooxihii daaweynta dabiiciga ah iyo duugis, fadhiyada Reflexology.
In daawaynta cudurada of dareenka weyn waa in la siiyo Axdigu chronic
caabuq ku yaal afka iyo bacaraarka (adenoids, chronic
qumanka, hogaga, ilkaha carious). daaweynta gaarka ah ee syndrome ilaa
Waxa aan la horumariyo. waafaqsan hab tur talinayo nolosha iyo sida
xakameyn kara on xamuulka jidhka. therapy Astaamaha ku lug saxo qalliinka ee cuuryaannimo thoracic, pseudotumour saarista, daaweynta heley isha, wadnaha, iwm Saadaalinta ah in nolosha inta badan ku xiran tahay nooca syndrome. Ka Hortagga waa la talinta hidaha.
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