CaafimaadkaCudurrada iyo Xaaladaha

Chorea - a ... chorea carruurta. chorea rheumatic

Chorea - cudurada ka mid ah habka dareemayaasha jirka. Waxaa loola jeedaa nooc oo hyperkinetic. cudurka waxaa ku weheliyay dhibaatooyinka la qanjidhada subcortical cerebral. Waxaa tilmaami karaa qaababka sifo: ah qiso, isug, shimbirka qasan ee gacmaha iyo cagaha, mararka qaarkood in jirridda. Marxaladaha dambe waxaa jira maskaxda iyo caqliga naafada ah, dhibaato isu-duwidda, iyo is-adeegga. Carruurta chorea inta badan waa qaldo hawlaha caadiga ah oo kordhay. Dhab ahaantii, marka calaamadaha ugu horeeya ee cudurka u baahan tahay in aad hesho kaalmo u qalma.

Ereyga "chorea"

Eraygan waxa loo isticmaalaa in laba xaaladood. Waxa loogu yeero laga yaabaa in cudurka madax banaan, kuwaas oo ka tirsan kooxda this (tus, chorea yar Huntington ama chorea). Sidoo kale waxaa la isticmaalaa in lagu tilmaamo syndromes qaarkood yimaadda marka noocyada kala duwan ee cudurrada. Erayga "chorea" ka luqada Giriigga, halkaas oo la tilmaamay by nooc ka mid ah qaar ka mid ah qoob ka yimaado. Tani waxay fasireysaa koowaad ee lagu garto, oo isu muujin in yaacday, midina, matago, dhaqdhaqaaqa degdeg ah oo ka mid ah jirrid iyo jirka. dhaqanka ee bukaanka waa run ahaantii sida aan ikhtiyaarka lahayn, qoob ka qasan. Beri baa la yiraahdo chorea "qoob ka St. Vitus ee." Magacani wuxuu ku xiran yahay la aaminsan hore ee St. Vitus, kaas oo si firfircoon uga faafi Masiixiyada, taas oo uu jirdilay by askari Roman. Ka dib markii uu dhintay ayaa noqday halyeey caan ah in haddii uu qof u qabtaan qoob ka firfircoon agagaarka qabrigiisa on dhalashadiisa, waxa uu heli doonaa lacag ah vivacity iyo tamarta ee sanadka oo dhan.

sababaha

Sababaha cudurka laga yaabaa in ay asal ahaan kala duwan, laakiin intooda badan chorea keeni arrimo dhaxaltooyo ama hiddo.

chorea ka yar caadiga ah, ay sababtay dabeecadda faafa sida cudurada sida meningitis TB, encephalitis viral, neurosyphilis, cudur ku faraxnay, xiiq-dheerta. Dhacdo of chorea la xidhiidha laga yaabaa in la kala dhantaalan dheefshiidka (haddii ay jiraan waa cudur Fabry ee, hyperglycemia, tayroodh, ama cudur Wilson ee), intiisa (khubad afka uurka, mercury, lithium, digoxin, neuroleptics, levodopa), heley, shalalka (sida antiphospholipid syndrome , lupus erythematosus oo nidaamsan, sclerosis). Ka mid ah sababaha ay ka cadhaysiiyaan dhacdo ee cudurka, dhakhaatiirta sidoo kale loo yaqaan dhismeedka maskaxda dhaawac. Waxaa ka mid ah formation buro, encephalopathy hypoxic, dhaawac maskaxda, stroke.

calaamadaha caadiga ah

Chorea - cudur muuqato random, fowdo, dhaqdhaqaaqa jirka waqti-gaaban. Xaaladaha qaarkood, dhaqdhaqaaqa, kuwaas oo la qaadi karaa si caadi ah, oo ku filan, la mid ah qof caafimaad qaba, wax ka welwelina. In dadka kale, waxay u eg dareen, qoob ka koontarooli karin. dhifasho matago noqon kartaa hal ama laba dhinac, laakiin iyagu ma ay leeyihiin ugu yaraan nooc ka mid ah synchronicity.

Iyada oo ku xidhan waxa foomka of cudurada helay, kala saaro calaamadaha chorea. Haddii qofka wax yar kaga hadlay hyperkinesis trochaic, ka dibna uu dhaqanka ayaa lagu arkay motor walaac yar, oo ay la socdaan disinhibition motor, kor u caadifinimadu, by mannerisms qaarkood, kuurkuursi, baaqyada aan habboonayn.

noocyada kala duwan Cad dhaqdhaqaqyo chorea hanti "yo-yo". qaab daran ee hyperkinesis trochaic xumeeyaan mooshinka ka mid ah socodka, hadalka iyo wajiga. wiiqmin bukaan-socodka la yaab leh ma aha oo kaliya, laakiin sidoo kale in qaar ka mid ah qiyaas "saxda". Chorea, calaamadaha mid ah kuwaas oo aad u adag, ma ogola xitaa qabtaan dhaqdhaqaaqa qaar ka mid ah. Bukaanka qaba cudurka daran ku xiran yihiin deegaanka, sida aysan u guurto iyo tiraan kartid naftaada nolosha buuxda.

Huntington ee chorea

cudurada Tani waxay u muuqato in kiisaska intooda badan ay da'doodu 35 ilaa 45 sanno u dhexeeya. Chorea, calaamadaha kuwaas oo, marka lagu daro hyperkinetic caadiga ah, qaado xanuunada shakhsiyadda dheeraad ah iyo dementia (hoos u dhac in sirdoonka) si tartiib tartiib ah uu yeesho, mararka qaarkood way adag tahay si loo raad joogo marka ay bilaabeen inay soo baxaan. The dhaqdhaqaaqa ugu horeysay rabshado dhacaan wajiga. Waxay waxaa lagu khaldaa automatisms motor random (carrabka this ridday, Yabaynaa, leefo bushimaha, afka furitaanka). Horumarka cudurka lagu muujiyey in horumarinta hyperkinetic ee jirridda iyo jirka. qaab daran gartaa doorin oo hadal, xusuusta, habka wax liqidda, heerka is-adeeg iyo dhamaado waallida qaba. Bilow for chorea Huntington ee cudurka dhimirka ee foomka of cudurada hallucinatory-khayaano, affective iyo dabeecadda.

Neyroakantotsitoz

bukaanka Neyroakantotsitozom xanuunsado hyperkinesis ma aha oo kaliya trochaic, laakiin acanthocytosis (isbedel sameeyaan unugyada dhiigga cas). Kala feature in cudurada tani waa atrophy (tabar in muruqyada jirka sare iyo hoose). Waxaa ka mid ah astaamaha kale ee la kala saaro cudurrada: hyperkinesis afka qaadka dhaqdhaqaaqa, gundhin dibinta ridday carrabka iyo wejiyo kale. Marka bukaanka neyroakantotsitoze qasab iskusyvaet uu carrabkiisa, dibnaha iyo daan in ay dusha hoose oo dhiigga. factor A complicating in cudurkan iyo dementia taag qalal.

Cudurka Lesch-macallimiinta Han

cudurada lagu dhasho ee habka dareemayaasha faragelin qof in ay ku noolaadaan nolol buuxda. heley Kuwani cudurrada la xiriira iyo Lesch-macallimiinta Han. Sababta ugu weyn ee cudurka waa deficiency ah dhaxlo ee hypoxanthine-gu'anayn. Tani chorea ee carruurta waxaa la socda rabshooyin halis dhaxgalka ee habka dareemayaasha jirka. Sidoo kale cudurada xanaajiyeen saarka sii kordhaya ee uric acid.

Laga soo bilaabo bilaha ugu horeeya ee nolosha ilmaha ayaa loo arkaa dib u dhac ah ee horumarinta. rigidity ee addimada ayaa lagu muujiyay bishii saddexaad. Laga soo bilaabo sannadkii labaad ee nolosha ilmaha isagoo grimaces wajiga, kuwaas oo ay la socdaan calaamadaha lesions mareenka pyramidal iyo dib u horumarka maskaxda. Baby jidh ahaan isu waxyeelayn kara by bushimahooda ayay ama faraha qaniinay.

chorea benign

Chorea caanood ee carruurta u muuqato in naaska ama carruurnimada hore. Pathology loola jeedaa cudurada la iska dhaxlo. hyperkinesia guud ee cudurkan Jeedsado kaliya marka ilmuhu hurdo. From chorea Huntington ee, noocan ah ee cudurada kala duwan waa non-progressors iyo horumarka caadiga ah ee sirdoonka. In jir ka weyn ee chorea benign Waxaad yarayn kartaa hyperkinetic, haddii waqtiga inaad la xiriirto xarunta caafimaad.

foomamka Dugsiga Sare ee chorea

Noocyada sare ugu badan ee cudurka waxaa loo arkaa laba: chorea iyo chorea ee uurka.

ugu horeeyay waxaa lagu magacaabaa Sydenhams ee. Iyada muuqaalka cadhaysiiyaan cudurka Streptococcus ba'an ama qandho rheumatic. foomka khafiif ah waxa lagu gartaa grimace buunbuuniyey, dhaqdhaqaajinta jirka dhegeysiga, dhaqdhaqaaqa disinhibition. Foomamka More adag oo hyperkinesis trochaic muujiyey in xaqiiqda ah in bukaan-socodka waa ay adag tahay in ay u guuraan, sida caadiga ah ku hadlin, xataa in aad neefsato. Marka cudurku ku dhacdaa sida jilbaha "tonic" iyo hummaag "dawayn", xanuunada dareenka iyo affective, hypertension muruqa ah.

chorea uurka leh - cudur la soo noqday laga soo bilaabo yaraantooda ay. Taasi waa, aaga khatarta ah waa uun kuwa dumarka ilmo qaba heesta yar kala kulantay. Pathology dhici kartaa inta ay uurka ugu horeysay ee 2-5 bilood. In koorsada ku xiga ee "oo xiiso leh" Xaaladda ayaa sidoo kale ka dhalan kara chorea. Daaweynta in kiisaska noocaas ah waa dhif iyo naadir, sida cudurka baaba'aa keligeed ka dib markii la dhexgelin ah ee uurka ama dhalmada ka dib.

rheumatica chorea

Dhacdooyinkaa cudurka imanaya xilli qandho korordhaysa rheumatic ama endocarditis, kaas oo la Ulasocto cudurka wadnaha valvular. kiisas badan oo cudurka ma la xiriira in arrin taasi, iyo cudurka madax banaan muuqato.

chorea Rheumatic inta badan saameeyaa caruurta da'doodu 6 iyo 15 sano u dhexeeya. In gabdhaha, cudurada ku badan yahay. Marxalada koowaad cudurka wuxuu noqon karaa sabab ah walaac, maxaa yeelay, calaamadaha waxaa ku koobnayn grimaces, iyo waalidiinta u qaadanayaa kaftan. Geedi socodka dhaqdhaqaaqyada aan ikhtiyaarka lahayn yar oo addimada ka, laga bilaabo suulasha iyo si tartiib tartiib ah oo fidsan laakiinse jidhka oo dhan. Toddobaad ka dib yimaado muddo dibad, markii dhaqdhaqaaqa ilmaha waa dhakhso ah oo dhulka xaadha. Xaaladani waxay ka hortagtaa ilmaha in ay sii wadaan hawlaha caadiga ah, in uu yahay, in la cuno, in ay socdaan, in ay qoraan.

chorea Rheumatic ay xumeeyaan wejiga ilmaha kumanyaal grimaces. noocyada halista ah ee cudurka faragelin bukaanka u istaagtid, si ay u liqi, in ay ku hadlaan, iyo jirka oo si joogto ah u dhaqaaqin. Haddii la chorea cudurka, daaweynta waa in la sameeyaa si fiican oo deg deg ah.

Baadhista xanuunada

chorea lagu tuhmay kici ay sabab u tahay dabeecad la yaab leh. In baaritaan horudhac ah, dhakhtarku waa in wada sheekeysi la bukaanka ama qoyskiisa. Gaar ahaan waxaa muhiim ah in la ogaado bal qof buka kale oo qoyska ka mid ah cudurkan, sida ay u dheer waxay ahaayeen calaamadaha chorea, in bukaanka qaatay daroogo, in cudurada bararka gaaray. takhasus dheeraad ah waa in la qiimeeyo dhaqdhaqaaq aan ikhtiyaarka lahayn. Waxa kale oo lagama maarmaan ah si loo soo ogaado oo sharaxaad ka mid ah cudurada la socon kartaa by chorea, keeni weecasho garaadka daran. Calaamadaha cudurada kuwaas oo aan had iyo jeer samayn Cad. Mararka qaarkood, si ay u ogaan aan caadi ahayn sida marxalad hore, adag oo ah waa la fuliyay sahan. baaritaanka dhiigga A tusi doonaa heerka copper dhiigga iyo joogitaanka ama maqnaanshaha of calaamadaha hawomareenka. Intaa waxaa dheer, u fuliyaan si raajito computer, magnetic resonance imaging, electroencephalography.

daaweynta

Chorea - cudurada ah in uusan u oggolaan in bukaanka si ay u qabtaan nolosha caadiga ah oo buuxa, sidaas darteed waa in la daaweeyaa in waqtigii a oo dhamaystiran. Khiyaamo daaweynta ku xiran tahay sababo cudur-kicinaya. Tusaale ahaan, in bukaanka cudurka Wilson ayaa qoray cunto la content ugu yar oo ah naxaas iyo daroogada, kuwaas oo ficil la faray at yaraynta ay nuugista.

Chorea Huntington qoray neuroleptics iyo dajiye Benzodiazepin. Haddii chorea sababa la'aan chronic ee socodka dhiigga maskaxda, waxaa loo baahan yahay daawooyinka hoos u cadaadiska dhiigga. Vaskulitis qaadeen daaweynta hormoon. Haddii aad ka muuqan calaamadaha aad guud, daawaynta waa in adag.

Iska yaree xoogga dhaqdhaqaaqa khasabka ah waa suurto gal by hab qalliin, markii baabbi'in xuduntii ventrolateral of thalamus ah. Chorea u baahan in ay qaataan daawo loo hagaajiyo hawlaha maskaxda iyo nafaqada, iyo sidoo kale vitamins ee group B.

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