CaafimaadkaCudurrada iyo Xaaladaha

Clinic Frederick syndrome

Frederick syndrome ay magaca helay oo lagu sharfayo physiologist Belgian ah, kuwaas oo waxaa lagu qeexaa sida isku-dar ah a transverse buuxa (atrioventikulyarnoy) go'doominta iyo wadne, in kiisaska kale - flutter wadne. Maqaalkani waxa uu ka hadlayaa Frederick syndrome: Tilmaamo clinical, iyo daaweynta cudurka.

farsamo syndrome

Frederick syndrome socda habab: ka atria si intraventricular gebi ahaanba istaago tabinta ee falalkooda, hagaagsanayn, fowdo, kicinta inta badan soo noqnoqda iyo yareynta kooxaha qaarkood macdantaa muruqa ah atria ah. intraventricular The ayaa aad ugu faraxsan pacemaker ah, oo ku yaalla nidaamka la xidhiidha ama tabinta atrioventricular.

Sababaha Frederick syndrome

Cudurku wuxuu ku dhici karaa ka dib markii lesions organic daran waxaa qalbiga ka, kuwaas oo inta badan la socda geedi socodka bararka, sclerotome ama xumaanshaha ee myocardium ah. Hababka noocaas ahi waxaa ka mid ah, tusaale ahaan, cudurada wadnaha ischaemic, inta badan ee foomka of chronic, Wadnaxanuun myocardial ba'an, myocarditis, cardiomyopathy, kog iyo kuwa kale. In cuduradan muruqa wadnaha horumariyaan geeddi socodka sclerotic, taasoo keentay in si aan loo baahneyn u fidiya nudaha connective, kaas oo badalay ah, unugyada jirka caadiga ah caadi in qaban kara dhaqdhaqaaqa korontada. Sidaa darteed, conductance waxaa carqaladeeyey, iyo uu jiro xanibaadda.

Waa maxay macnaha cardiogram ah

Si loo xaqiijiyo bukaanka syndrome Frederick, sida caadiga ah, electrocardiograms dhaqanka ay maamusho. Waxaa intaa dheer, daraasad ku qaadeen maalmo ka fiican si ay u qiimeeyaan xaddiga garaaca wadnaha waqtiyo kala duwan iyo si ay u ururiyaan macluumaad dheeraad ah.

In jiritaanka cudurka on hirarka ECG waxaa lagu duubay aamba ama flutter wadne, halka qof caafimaad qaba waa in ay leeyihiin ilkaha. laxanka Ventricular noqdo xarun ama idioventricular, iyo guud ahaan - nesinusovym ectopic. dura RR waa joogto ah oo ay leeyihiin laxanka saxda ah. Tirada heerka ventricular diiwaan geliyay lacagta aan ka badnayn 50-60 jeer daqiiqadiiba. kaxeynayo Ventricular inta badan waa la weyneyn iyo maroorsamaan.

calaamadaha iyo astaamaha Clinical

iyadoo la kaashanayo electrocardiogram ah oo keliya si sax xaqiijin karaa bukaanka Frederick syndrome. Clinic, isaga raacsan nolol maalmeedka, taas oo ah in ay soo jiidan doonaan dareenka qofka - waa dhif, laakiin heerka wadnaha midig ku garaaca wadnaha ka mid ah ugu yaraan 30 iyo in aan ka badnayn 60 jeer daqiiqadiiba. heerka garaaca wadnaha lagu dhibciyo sababtoo ah shaqo shubto hoos qalbiga ku. Taa baddalkeeda, kor ku xusan waxay keenaysaa in gaajo ogsijiin of maskaxda.

Bukaanka inta badan ka caban of tabar, wareer, neefta oo ku qabata, sii xumaanaysa ee caafimaadka xitaa ka dib markii wax yar jimicsi ah. Haddii qofku uusan bixin si Frederick ee syndrome dareenka, calaamadaha waxaa sii xumeeyey, ayaa laga yaabaa inuu wadnaha waarta 5-7 ilbiriqsi. Intaa waxaa dheer, waxaa laga yaabaa in miyirka oo luma sabab u tachycardia ventricular.

daaweynta

Sii kordheysa, dhakhaatiirta isku raacsan yihiin in xalka kaliya ee saxda ah ee daaweynta ee Frederick syndrome waa galinta ee pacemaker macmal ah. In la gelinayaa koronto ventricle ah, taas oo ka samatabbixiyaa karsado iyo kiimikaysan keena foosha ee myocardium ah. Inta jeer ee foosha ayaa lagu wadaa ka hor ku xiran xaaladda bukaanka iyo dhaqdhaqaaqa jirka.

Waxa intaa dheer in laso- iyo isticmaali holinoblokatory. Macluumaadkaan waxaa gaar ah, sida atropine. Recently, si kastaba ha ahaatee, codsigooda diiday sababtoo ah waxyeelo badan, oo ay ku jiraan saameyn xun ku soo gunaanadeen ee bukaanka, tusaale ahaan, horumarinta psychosis atropinovogo.

Guud ahaan, daaweynta ku xiran tahay xasiloonida ee hemodynamics iyo sababaha go'doominta atrioventikulyarnoy.

Sayidka, Frederick syndrome waa darantahay ku filan si ay u jabiyaan muruqa wadnaha, lagu gartaa total Go'doominta transverse isku dhafan oo wadne.

Currently, si kastaba ha ahaatee, iyadoo cudurka habboon iyo waqtiga loogu talagalay this ifafaale waa la daaweyn karaa, ka dib markii taas oo qofka bukaanka ah ku noqon karto caadi ah iyo dayactirka jidkooda dhaqanka ee nolosha.

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